Departments of Endocrinology (A.J.L.C.), St. Bartholomew’s and the
Royal London School of Medicine and Dentistry, West Smithfield, London
EC1A 7BE, United Kingdom; and Children’s Hospital (A.W.), Technical
University Dresden, D-01307 Dresden, Germany
I. Introduction
II. Familial Glucocorticoid Deficiency
A.Clinical presentation
B. Investigation
C. Treatment
D.Pathogenesis
III. Triple A Syndrome
A. Clinical features
B. Treatment
C. Pathogenesis
D. Mapping of triple A syndromegene
E. Candidate genes
IV. Acquired ACTH Resistance
V.Conclusions
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